Actualización en hipertensión pulmonar pediátrica

Cantirán, K., Moreira, I., & Pinchak, C. (2026). Update: pediatric pulmonary hypertension. Archives of Pediatrics of Uruguay, 97(1), e603. https://doi.org/10.31134/AP.97.1.16

Abstract

Pulmonary hypertension (PH) is a rare entity. It is not a disease in itself, but a heterogeneous hemodynamic and pathophysiological state that results from various clinical conditions. PH is classified into five groups, from 1 to 5. In pediatrics, the most frequent groups are 1 and 3. Early diagnosis is essential to enable timely treatment, slowing the remodeling of pulmonary vessels and cardiac chambers, and preventing the development of Cor pulmonale.

https://doi.org/10.31134/AP.97.1.16

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